Diagnosis and Management of Progressive Pulmonary Fibrosis (PPF)

Fibrotic lung disease is a group of around 200 entities that have inflammation and/or fibrosis in common. The “progressive” phenotype of pulmonary fibrosis has recently become more well-defined. Tejaswini Kulkarni, M.D., explains the characteristics of progressive pulmonary fibrosis (PPF). She discusses the importance of recognizing when interstitial lung disease is indeed PPF and addressing it with a combination of immunosuppressive and antifibrotic therapies. Learn about the advantages of interdisciplinary care for patients with PPF, including early recognition and management of worsening lung function; use of pulmonary rehabilitation and supplemental oxygen for better quality of life; and walking patients through the lung transplant process when necessary.